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Open Access
Peer-reviewed
Research Article
Evaluating protein cross-linking as a therapeutic strategy to stabilize SOD1 variants in a mouse model of familial ALS
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Md Amin Hossain ,
Contributed equally to this work with: Md Amin Hossain, Richa Sarin
Roles Conceptualization, Data curation, Formal analysis, Methodology, Software, Validation, Visualization, Writing – original draft, Writing – review & editing
Affiliations Department of Chemistry and Chemical Biology, Northeastern University, Boston, Massachusetts, United States of America, Barnett Institute of Chemical and Biological Analysis, Boston, Massachusetts, United States of America, Department of Neurosurgery and Department of Radiology, Brigham and Women’s Hospital, Harvard Medical School, Boston, Massachusetts, United States of America
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Richa Sarin ,
Contributed equally to this work with: Md Amin Hossain, Richa Sarin
Roles Conceptualization, Data curation, Formal analysis, Methodology, Software, Validation, Visualization, Writing – original draft, Writing – review & editing
Affiliations Department of Chemistry and Chemical Biology, Northeastern University, Boston, Massachusetts, United States of America, Biogen Inc, Cambridge, Massachusetts, United States of America
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Daniel P. Donnelly,
Roles Conceptualization, Data curation, Formal analysis, Methodology, Software, Validation, Visualization, Writing – original draft
Affiliations Department of Chemistry and Chemical Biology, Northeastern University, Boston, Massachusetts, United States of America, Barnett Institute of Chemical and Biological Analysis, Boston, Massachusetts, United States of America
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Brandon C. Miller,
Roles Data curation, Formal analysis, Methodology, Software, Validation, Visualization, Writing – original draft
Affiliation Department of Chemistry and Chemical Biology, Northeastern University, Boston, Massachusetts, United States of America
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Alexandra Weiss,
Roles Data curation, Formal analysis, Methodology, Software, Validation, Visualization, Writing – original draft, Writing – review & editing
Affiliation Department of Neurology, University of Massachusetts Medical School, Worcester, Massachusetts, United States of America
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Luke McAlary,
Roles Data curation, Formal analysis, Methodology, Software, Validation, Visualization, Writing – original draft, Writing – review & editing
Affiliation Molecular Horizons and School of Chemistry and Molecular Bioscience, University of Wollongong, Wollongong, Australia
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Svetlana V. Antonyuk,
Roles Data curation, Formal analysis, Methodology, Software, Validation, Visualization, Writing – original draft, Writing – review & editing
Affiliation Molecular Biophysics Group, Department of Biochemistry & Systems Biology, Faculty of Health and Life Sciences, University of Liverpool, Liverpool, United Kingdom
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Joseph P. Salisbury,
Roles Conceptualization, Data curation, Formal analysis, Methodology, Software, Validation, Visualization, Writing – original draft
Affiliation Department of Chemistry and Chemical Biology, Northeastern University, Boston, Massachusetts, United States of America
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Jakal Amin,
Roles Data curation, Formal analysis, Methodology, Software, Visualization
Affiliations Department of Chemistry and Chemical Biology, Northeastern University, Boston, Massachusetts, United States of America, Barnett Institute of Chemical and Biological Analysis, Boston, Massachusetts, United States of America
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Jeremy B. Conway,
Roles Data curation, Formal analysis, Methodology, Writing – original draft
Affiliation Department of Chemistry and Chemical Biology, Northeastern University, Boston, Massachusetts, United States of America
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Samantha S. Watson,
Roles Data curation, Formal analysis, Methodology, Software, Validation, Visualization, Writing – original draft
Affiliation Department of Chemistry and Chemical Biology, Northeastern University, Boston, Massachusetts, United States of America
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Jenifer N. Winters,
Roles Data curation, Formal analysis, Methodology, Software, Validation, Visualization, Writing – original draft
Affiliation Department of Chemistry and Chemical Biology, Northeastern University, Boston, Massachusetts, United States of America
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Yu Xu,
Roles Data curation, Formal analysis, Methodology, Software, Validation, Visualization, Writing – original draft
Affiliation Department of Pharmaceutical Sciences, Northeastern University, Boston, Massachusetts, United States of America
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Novera Alam,
Roles Data curation, Formal analysis, Methodology, Software, Validation, Visualization, Writing – original draft
Affiliations Department of Chemistry and Chemical Biology, Northeastern University, Boston, Massachusetts, United States of America, Barnett Institute of Chemical and Biological Analysis, Boston, Massachusetts, United States of America
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Rutali R. Brahme,
Roles Data curation, Formal analysis
Affiliations Department of Chemistry and Chemical Biology, Northeastern University, Boston, Massachusetts, United States of America, Barnett Institute of Chemical and Biological Analysis, Boston, Massachusetts, United States of America
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Haneyeh Shahbazian,
Roles Data curation
Affiliation School of Medicine, University of North Carolina, Chapel Hill, North Carolina, United States of America
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Durgalakshmi Sivasankar,
Roles Data curation, Formal analysis
Affiliations Department of Chemistry and Chemical Biology, Northeastern University, Boston, Massachusetts, United States of America, Barnett Institute of Chemical and Biological Analysis, Boston, Massachusetts, United States of America
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Swathi Padmakumar,
Roles Data curation
Affiliation Department of Chemistry and Chemical Biology, Northeastern University, Boston, Massachusetts, United States of America
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Aziza Sattarova,
Roles Data curation, Formal analysis
Affiliation Department of Pharmaceutical Sciences, Northeastern University, Boston, Massachusetts, United States of America
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Aparna C. Ponmudiyan,
Roles Data curation
Affiliation Department of Chemistry and Chemical Biology, Northeastern University, Boston, Massachusetts, United States of America
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Tanvi Gawde,
Roles Data curation
Affiliation Department of Chemistry and Chemical Biology, Northeastern University, Boston, Massachusetts, United States of America
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David E. Verrill,
Roles Data curation, Formal analysis, Software, Visualization, Writing – review & editing
Affiliations Department of Chemistry and Chemical Biology, Northeastern University, Boston, Massachusetts, United States of America, Barnett Institute of Chemical and Biological Analysis, Boston, Massachusetts, United States of America
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Wensheng Yang,
Roles Data curation
Affiliations Department of Chemistry and Chemical Biology, Northeastern University, Boston, Massachusetts, United States of America, Barnett Institute of Chemical and Biological Analysis, Boston, Massachusetts, United States of America
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Sunanda Kannapadi,
Roles Data curation
Affiliation Department of Chemistry and Chemical Biology, Northeastern University, Boston, Massachusetts, United States of America
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Leigh D. Plant,
Roles Investigation, Methodology, Resources, Software, Supervision, Validation, Visualization, Writing – original draft
Affiliation Department of Pharmaceutical Sciences, Northeastern University, Boston, Massachusetts, United States of America
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Jared R. Auclair,
Roles Investigation, Resources, Supervision
Affiliations Department of Chemistry and Chemical Biology, Northeastern University, Boston, Massachusetts, United States of America, Barnett Institute of Chemical and Biological Analysis, Boston, Massachusetts, United States of America
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Lee Makowski,
Roles Investigation, Methodology, Software, Supervision, Validation
Affiliations Department of Chemistry and Chemical Biology, Northeastern University, Boston, Massachusetts, United States of America, Department of Bioengineering, Northeastern University, Boston, Massachusetts, United States of America
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Gregory A. Petsko,
Roles Investigation, Supervision, Validation
Affiliations Ann Romney Center for Neurologic Diseases at Brigham and Women’s Hospital, Harvard Medical School, Boston, Massachusetts, United States of America, Departments of Chemistry and Biochemistry, and Rosenstiel Center for Basic Medical Research, Brandeis University, Waltham, Massachusetts, United States of America
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Dagmar Ringe,
Roles Investigation, Supervision
Affiliation Departments of Chemistry and Biochemistry, and Rosenstiel Center for Basic Medical Research, Brandeis University, Waltham, Massachusetts, United States of America
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Nathalie Y. R. Agar,
Roles Investigation, Resources, Supervision, Writing – review & editing
Affiliations Department of Neurosurgery and Department of Radiology, Brigham and Women’s Hospital, Harvard Medical School, Boston, Massachusetts, United States of America, Department of Cancer Biology, Dana-Farber Cancer Institute, Harvard Medical School, Boston, Massachusetts, United States of America
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David J. Greenblatt,
Roles Investigation, Resources, Supervision
Affiliation School of Medicine, Tufts University, Boston, Massachusetts, United States of America
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Mary Jo Ondrechen,
Roles Conceptualization, Formal analysis, Investigation, Methodology, Resources, Software, Supervision, Validation, Visualization, Writing – original draft, Writing – review & editing
Affiliation Department of Chemistry and Chemical Biology, Northeastern University, Boston, Massachusetts, United States of America
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Yunqiu Chen,
Roles Investigation, Resources, Supervision, Validation
Affiliation Biogen Inc, Cambridge, Massachusetts, United States of America
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Justin J. Yerbury,
Roles Formal analysis, Investigation, Methodology, Resources, Software, Supervision, Validation, Visualization, Writing – original draft
Affiliation Molecular Horizons and School of Chemistry and Molecular Bioscience, University of Wollongong, Wollongong, Australia
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Roman Manetsch,
Roles Conceptualization, Formal analysis, Investigation, Methodology, Resources, Software, Supervision, Validation, Visualization, Writing – original draft, Writing – review & editing
Affiliations Department of Chemistry and Chemical Biology, Northeastern University, Boston, Massachusetts, United States of America, Department of Pharmaceutical Sciences, Northeastern University, Boston, Massachusetts, United States of America
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S. Samar Hasnain,
Roles Formal analysis, Investigation, Methodology, Resources, Software, Supervision, Validation, Visualization, Writing – original draft, Writing – review & editing
Affiliation Molecular Biophysics Group, Department of Biochemistry & Systems Biology, Faculty of Health and Life Sciences, University of Liverpool, Liverpool, United Kingdom
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Robert H. Brown Jr.,
Roles Investigation, Methodology, Resources, Supervision, Validation, Writing – original draft
Affiliation Department of Neurology, University of Massachusetts Medical School, Worcester, Massachusetts, United States of America
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Jeffrey N. Agar
Roles Conceptualization, Data curation, Formal analysis, Investigation, Methodology, Resources, Software, Supervision, Validation, Visualization, Writing – original draft, Writing – review & editing
* E-mail: j.agar@northeastern.edu
Affiliations Department of Chemistry and Chemical Biology, Northeastern University, Boston, Massachusetts, United States of America, Barnett Institute of Chemical and Biological Analysis, Boston, Massachusetts, United States of America, Department of Pharmaceutical Sciences, Northeastern University, Boston, Massachusetts, United States of America
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Evaluating protein cross-linking as a therapeutic strategy to stabilize SOD1 variants in a mouse model of familial ALS
- Md Amin Hossain,
- Richa Sarin,
- Daniel P. Donnelly,
- Brandon C. Miller,
- Alexandra Weiss,
- Luke McAlary,
- Svetlana V. Antonyuk,
- Joseph P. Salisbury,
- Jakal Amin,
- Jeremy B. Conway
- Published: January 30, 2024
- https://doi.org/10.1371/journal.pbio.3002462