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Open Access
Peer-reviewed
Research Article
A fly model of SCA36 reveals combinatorial neurotoxicity of hexanucleotide and dipeptide repeats
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Cheng-Tsung Hsiao,
Roles Data curation, Formal analysis, Methodology, Writing – original draft
Affiliations Graduate Institute of Physiology, National Taiwan University, Taipei, Taiwan, Department of Neurology, National Yang Ming Chiao Tung University School of Medicine, Taipei, Taiwan, Department of Neurology, Neurological Institute, Taipei Veterans General Hospital, Taipei, Taiwan
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Ssu-Ju Fu,
Roles Conceptualization, Data curation, Formal analysis, Investigation, Methodology, Validation, Visualization, Writing – original draft
Affiliations Graduate Institute of Physiology, National Taiwan University, Taipei, Taiwan, Department of Neurology, Neurological Institute, Taipei Veterans General Hospital, Taipei, Taiwan, School of Medicine, Fu‑Jen Catholic University, New Taipei City, Taiwan
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Ting-Ni Guo,
Roles Conceptualization, Data curation, Formal analysis, Investigation, Methodology, Validation, Visualization, Writing – original draft
Affiliations Graduate Institute of Physiology, National Taiwan University, Taipei, Taiwan, Department of Neurology, Neurological Institute, Taipei Veterans General Hospital, Taipei, Taiwan
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Chia-Chi Lin,
Roles Investigation, Methodology
Affiliation Institute of Basic Medical Sciences, College of Medicine, National Cheng Kung University, Tainan, Taiwan
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Yu-Jung Tsao,
Roles Data curation, Formal analysis, Investigation, Methodology, Validation, Writing – original draft
Affiliations Graduate Institute of Physiology, National Taiwan University, Taipei, Taiwan, Department of Neurology, Neurological Institute, Taipei Veterans General Hospital, Taipei, Taiwan
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Wenying Chang,
Roles Data curation, Investigation, Methodology
Affiliations Graduate Institute of Physiology, National Taiwan University, Taipei, Taiwan, Department of Neurology, Neurological Institute, Taipei Veterans General Hospital, Taipei, Taiwan
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Yi-Chu Liao,
Roles Investigation, Writing – original draft
Affiliations Department of Neurology, National Yang Ming Chiao Tung University School of Medicine, Taipei, Taiwan, Department of Neurology, Neurological Institute, Taipei Veterans General Hospital, Taipei, Taiwan, Brain Research Center, National Yang Ming Chiao Tung University School of Medicine, Taipei, Taiwan
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Masayuki Hashimoto,
Roles Investigation, Methodology
Affiliations Institute of Basic Medical Sciences, College of Medicine, National Cheng Kung University, Tainan, Taiwan, Institute of Molecular Medicine, College of Medicine, National Cheng Kung University, Tainan, Taiwan
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Shu-Yi Huang,
Roles Methodology, Validation, Writing – original draft
Affiliation Department of Medical Research, National Taiwan University Hospital, Taipei, Taiwan
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Yi-Chung Lee,
Roles Investigation, Writing – original draft
Affiliations Department of Neurology, National Yang Ming Chiao Tung University School of Medicine, Taipei, Taiwan, Department of Neurology, Neurological Institute, Taipei Veterans General Hospital, Taipei, Taiwan, Brain Research Center, National Yang Ming Chiao Tung University School of Medicine, Taipei, Taiwan
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Chien-Hung Yu ,
Roles Conceptualization, Funding acquisition, Methodology, Writing – original draft, Writing – review & editing
* E-mail: chancc1@ntu.edu.tw (C-CC); chienhung_yu@mail.ncku.edu.tw (C-HY)
Affiliations Institute of Basic Medical Sciences, College of Medicine, National Cheng Kung University, Tainan, Taiwan, Department of Biochemistry and Molecular Biology, College of Medicine, National Cheng Kung University, Tainan, Taiwan
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Chih-Chiang Chan
Roles Conceptualization, Funding acquisition, Methodology, Writing – original draft, Writing – review & editing
* E-mail: chancc1@ntu.edu.tw (C-CC); chienhung_yu@mail.ncku.edu.tw (C-HY)
Affiliation Graduate Institute of Physiology, National Taiwan University, Taipei, Taiwan
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A fly model of SCA36 reveals combinatorial neurotoxicity of hexanucleotide and dipeptide repeats
- Cheng-Tsung Hsiao,
- Ssu-Ju Fu,
- Ting-Ni Guo,
- Chia-Chi Lin,
- Yu-Jung Tsao,
- Wenying Chang,
- Yi-Chu Liao,
- Masayuki Hashimoto,
- Shu-Yi Huang,
- Yi-Chung Lee
- Published: December 3, 2025
- https://doi.org/10.1371/journal.pgen.1011954