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Open Access
Peer-reviewed
Research Article
Schwann cells ER-associated degradation contributes to myelin maintenance in adult nerves and limits demyelination in CMT1B mice
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Vera G. Volpi,
Roles Data curation, Formal analysis, Investigation, Methodology, Validation, Writing – original draft, Writing – review & editing
Affiliation Division of Genetics and Cell Biology, IRCCS San Raffaele Scientific Institute, Milan, Italy
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Cinzia Ferri,
Roles Investigation, Methodology, Validation
Affiliation Division of Genetics and Cell Biology, IRCCS San Raffaele Scientific Institute, Milan, Italy
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Ilaria Fregno,
Roles Investigation, Methodology
Affiliations Instuitute for Research in Biomedicine, Faculty of Biomedical Sciences, Università della Svizzera italiana (USI), Bellinzona, Switzerland, Department of Biology, Swiss Federal Institute of Technology, Zurich, Switzerland
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Ubaldo Del Carro,
Roles Investigation, Methodology
Affiliation Institute of Experimental Neurology (INSPE), Division of Neuroscience, IRCCS San Raffaele Scientific Institute, Milan, Italy
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Francesca Bianchi,
Roles Investigation, Methodology
Affiliation Institute of Experimental Neurology (INSPE), Division of Neuroscience, IRCCS San Raffaele Scientific Institute, Milan, Italy
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Cristina Scapin,
Roles Formal analysis, Investigation
Affiliation Division of Genetics and Cell Biology, IRCCS San Raffaele Scientific Institute, Milan, Italy
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Emanuela Pettinato,
Roles Investigation, Methodology
Affiliation Division of Genetics and Cell Biology, IRCCS San Raffaele Scientific Institute, Milan, Italy
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Tatiana Solda,
Roles Investigation, Methodology
Affiliation Instuitute for Research in Biomedicine, Faculty of Biomedical Sciences, Università della Svizzera italiana (USI), Bellinzona, Switzerland
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M. Laura Feltri,
Roles Resources
Affiliations Hunter James Kelly Research Institute, University at Buffalo, Buffalo, New York, United States of America, Department of Neurology, Jacobs School of Medicine and Biomedical Sciences, University at Buffalo, Buffalo, New York, United States of America, Department of Biochemistry, Jacobs School of Medicine and Biomedical Sciences, University at Buffalo, Buffalo, New York, United States of America
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Maurizio Molinari,
Roles Investigation, Methodology, Resources
Affiliations Instuitute for Research in Biomedicine, Faculty of Biomedical Sciences, Università della Svizzera italiana (USI), Bellinzona, Switzerland, School of Life Sciences, École Polytechnique Fédérale de Lausanne, Lausanne, Switzerland
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Lawrence Wrabetz,
Roles Resources
Affiliations Hunter James Kelly Research Institute, University at Buffalo, Buffalo, New York, United States of America, Department of Neurology, Jacobs School of Medicine and Biomedical Sciences, University at Buffalo, Buffalo, New York, United States of America, Department of Biochemistry, Jacobs School of Medicine and Biomedical Sciences, University at Buffalo, Buffalo, New York, United States of America
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Maurizio D’Antonio
Roles Conceptualization, Data curation, Formal analysis, Funding acquisition, Methodology, Project administration, Supervision, Validation, Writing – original draft, Writing – review & editing
* E-mail: dantonio.maurizio@hsr.it
Affiliation Division of Genetics and Cell Biology, IRCCS San Raffaele Scientific Institute, Milan, Italy
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Schwann cells ER-associated degradation contributes to myelin maintenance in adult nerves and limits demyelination in CMT1B mice
- Vera G. Volpi,
- Cinzia Ferri,
- Ilaria Fregno,
- Ubaldo Del Carro,
- Francesca Bianchi,
- Cristina Scapin,
- Emanuela Pettinato,
- Tatiana Solda,
- M. Laura Feltri,
- Maurizio Molinari
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- Published: April 17, 2019
- https://doi.org/10.1371/journal.pgen.1008069