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Open Access
Peer-reviewed
Research Article
Bioenergetic status modulates motor neuron vulnerability and pathogenesis in a zebrafish model of spinal muscular atrophy
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Penelope J. Boyd,
Affiliations Euan MacDonald Centre for Motor Neurone Disease Research, University of Edinburgh, Edinburgh, United Kingdom, Centre for Integrative Physiology, Edinburgh Medical School: Biomedical Sciences, University of Edinburgh, Edinburgh, United Kingdom
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Wen-Yo Tu,
Affiliation Sheffield Institute for Translation Neuroscience, University of Sheffield, Sheffield, United Kingdom
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Hannah K. Shorrock,
Affiliations Euan MacDonald Centre for Motor Neurone Disease Research, University of Edinburgh, Edinburgh, United Kingdom, Centre for Integrative Physiology, Edinburgh Medical School: Biomedical Sciences, University of Edinburgh, Edinburgh, United Kingdom
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Ewout J. N. Groen,
Affiliations Euan MacDonald Centre for Motor Neurone Disease Research, University of Edinburgh, Edinburgh, United Kingdom, Centre for Integrative Physiology, Edinburgh Medical School: Biomedical Sciences, University of Edinburgh, Edinburgh, United Kingdom
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Roderick N. Carter,
Affiliation University/British Heart Foundation Centre for Cardiovascular Science, University of Edinburgh, Queens Medical Research Institute, Edinburgh, United Kingdom
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Rachael A. Powis,
Affiliations Euan MacDonald Centre for Motor Neurone Disease Research, University of Edinburgh, Edinburgh, United Kingdom, Centre for Integrative Physiology, Edinburgh Medical School: Biomedical Sciences, University of Edinburgh, Edinburgh, United Kingdom
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Sophie R. Thomson,
Affiliation Centre for Integrative Physiology, Edinburgh Medical School: Biomedical Sciences, University of Edinburgh, Edinburgh, United Kingdom
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Derek Thomson,
Affiliation Centre for Integrative Physiology, Edinburgh Medical School: Biomedical Sciences, University of Edinburgh, Edinburgh, United Kingdom
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Laura C. Graham,
Affiliation Division of Neurobiology, Roslin Institute, University of Edinburgh, Edinburgh, United Kingdom
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Anna A. L. Motyl,
Affiliation Centre for Integrative Physiology, Edinburgh Medical School: Biomedical Sciences, University of Edinburgh, Edinburgh, United Kingdom
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Thomas M. Wishart,
Affiliation Division of Neurobiology, Roslin Institute, University of Edinburgh, Edinburgh, United Kingdom
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J. Robin Highley,
Affiliation Sheffield Institute for Translation Neuroscience, University of Sheffield, Sheffield, United Kingdom
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Nicholas M. Morton,
Affiliation University/British Heart Foundation Centre for Cardiovascular Science, University of Edinburgh, Queens Medical Research Institute, Edinburgh, United Kingdom
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Thomas Becker,
Affiliations Euan MacDonald Centre for Motor Neurone Disease Research, University of Edinburgh, Edinburgh, United Kingdom, Centre for Neuroregeneration, Edinburgh Medical School: Biomedical Sciences, University of Edinburgh, Edinburgh, United Kingdom
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Catherina G. Becker,
Affiliations Euan MacDonald Centre for Motor Neurone Disease Research, University of Edinburgh, Edinburgh, United Kingdom, Centre for Neuroregeneration, Edinburgh Medical School: Biomedical Sciences, University of Edinburgh, Edinburgh, United Kingdom
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Paul R. Heath,
Affiliation Sheffield Institute for Translation Neuroscience, University of Sheffield, Sheffield, United Kingdom
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Thomas H. Gillingwater
* E-mail: T.Gillingwater@ed.ac.uk
Affiliations Euan MacDonald Centre for Motor Neurone Disease Research, University of Edinburgh, Edinburgh, United Kingdom, Centre for Integrative Physiology, Edinburgh Medical School: Biomedical Sciences, University of Edinburgh, Edinburgh, United Kingdom
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Bioenergetic status modulates motor neuron vulnerability and pathogenesis in a zebrafish model of spinal muscular atrophy
- Penelope J. Boyd,
- Wen-Yo Tu,
- Hannah K. Shorrock,
- Ewout J. N. Groen,
- Roderick N. Carter,
- Rachael A. Powis,
- Sophie R. Thomson,
- Derek Thomson,
- Laura C. Graham,
- Anna A. L. Motyl
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- Published: April 20, 2017
- https://doi.org/10.1371/journal.pgen.1006744