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Open Access
Peer-reviewed
Research Article
Abnormal Brain Iron Metabolism in Irp2 Deficient Mice Is Associated with Mild Neurological and Behavioral Impairments
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Kimberly B. Zumbrennen-Bullough,
Affiliation Program in Anemia Signaling Research, Division of Nephrology, Program in Membrane Biology, Center for Systems Biology, Massachusetts General Hospital, Harvard Medical School, Boston, Massachusetts, United States of America
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Lore Becker,
Affiliations German Mouse Clinic, Helmholtz-Zentrum München, German Research Center for Environmental Health, Neuherberg, Germany, Institute of Experimental Genetics, Helmholtz-Zentrum München, German Research Center for Environmental Health, Neuherberg, Germany
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Lillian Garrett,
Affiliations German Mouse Clinic, Helmholtz-Zentrum München, German Research Center for Environmental Health, Neuherberg, Germany, Institute of Development Genetics, Helmholtz-Zentrum München, German Research Center for Environmental Health, Neuherberg, Germany
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Sabine M. Hölter,
Affiliations German Mouse Clinic, Helmholtz-Zentrum München, German Research Center for Environmental Health, Neuherberg, Germany, Institute of Development Genetics, Helmholtz-Zentrum München, German Research Center for Environmental Health, Neuherberg, Germany
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Julia Calzada-Wack,
Affiliations German Mouse Clinic, Helmholtz-Zentrum München, German Research Center for Environmental Health, Neuherberg, Germany, Institute of Pathology, Helmholtz-Zentrum München, German Research Center for Environmental Health, Neuherberg, Germany
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Ilona Mossbrugger,
Affiliations German Mouse Clinic, Helmholtz-Zentrum München, German Research Center for Environmental Health, Neuherberg, Germany, Institute of Pathology, Helmholtz-Zentrum München, German Research Center for Environmental Health, Neuherberg, Germany
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Leticia Quintanilla-Fend,
Affiliations German Mouse Clinic, Helmholtz-Zentrum München, German Research Center for Environmental Health, Neuherberg, Germany, Institute of Pathology, Helmholtz-Zentrum München, German Research Center for Environmental Health, Neuherberg, Germany
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Ildiko Racz,
Affiliations German Mouse Clinic, Helmholtz-Zentrum München, German Research Center for Environmental Health, Neuherberg, Germany, Institute of Molecular Psychiatry, Life & Brain Center, University of Bonn, Bonn, Germany
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Birgit Rathkolb,
Affiliations German Mouse Clinic, Helmholtz-Zentrum München, German Research Center for Environmental Health, Neuherberg, Germany, Institute of Molecular Animal Breeding and Biotechnology, Gene Center, Ludwig-Maximilians-Universitat, Munich, Germany
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Thomas Klopstock,
Affiliations Department of Neurology, Friedrich-Baur-Institute, Klinikum der Ludwig-Maximilians-Universitat, Munich, Germany, Deutsches Zentrum für Neurodegenerative Erkrankungen, Munich, Germany, Munich Cluster for Systems Neurology, Munich, Germany
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Wolfgang Wurst,
Affiliations Institute of Development Genetics, Helmholtz-Zentrum München, German Research Center for Environmental Health, Neuherberg, Germany, Chair of Developmental Genetics, Technische Universitat München, Freising-Weihenstephan, Germany, Max Planck Institute of Psychiatry, Munich, Germany, Deutsches Zentrum für Neurodegenerative Erkrankungen, Munich, Germany, Munich Cluster for Systems Neurology, Munich, Germany
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Andreas Zimmer,
Affiliation Institute of Molecular Psychiatry, Life & Brain Center, University of Bonn, Bonn, Germany
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Eckhard Wolf,
Affiliation Institute of Molecular Animal Breeding and Biotechnology, Gene Center, Ludwig-Maximilians-Universitat, Munich, Germany
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Helmut Fuchs,
Affiliations German Mouse Clinic, Helmholtz-Zentrum München, German Research Center for Environmental Health, Neuherberg, Germany, Institute of Experimental Genetics, Helmholtz-Zentrum München, German Research Center for Environmental Health, Neuherberg, Germany
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Valerie Gailus-Durner,
Affiliations German Mouse Clinic, Helmholtz-Zentrum München, German Research Center for Environmental Health, Neuherberg, Germany, Institute of Experimental Genetics, Helmholtz-Zentrum München, German Research Center for Environmental Health, Neuherberg, Germany
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Martin Hrabě de Angelis,
Affiliations German Mouse Clinic, Helmholtz-Zentrum München, German Research Center for Environmental Health, Neuherberg, Germany, Institute of Experimental Genetics, Helmholtz-Zentrum München, German Research Center for Environmental Health, Neuherberg, Germany, Chair of Experimental Genetics, Center of Life and Food Sciences Weihenstephan, Technische Universitat München, Freising, Germany, German Center for Diabetes Research, Neuherberg, Germany
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Steven J. Romney,
Affiliation University of Utah, Department of Medicine, Division of Hematology and Hematological Malignancies, Salt Lake City, Utah, United States of America
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Elizabeth A. Leibold
* E-mail: betty.leibold@genetics.utah.edu
Affiliation University of Utah, Department of Medicine, Division of Hematology and Hematological Malignancies, Salt Lake City, Utah, United States of America
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Abnormal Brain Iron Metabolism in Irp2 Deficient Mice Is Associated with Mild Neurological and Behavioral Impairments
- Kimberly B. Zumbrennen-Bullough,
- Lore Becker,
- Lillian Garrett,
- Sabine M. Hölter,
- Julia Calzada-Wack,
- Ilona Mossbrugger,
- Leticia Quintanilla-Fend,
- Ildiko Racz,
- Birgit Rathkolb,
- Thomas Klopstock
- Published: June 4, 2014
- https://doi.org/10.1371/journal.pone.0098072