Fig 1.
Average hearing thresholds of Fabry Patients and healthy individuals, based on age and sex.
The top two diagrams show the mean hearing thresholds of both ears in dB for Fabry patients at frequencies from 0.25 kHz-8 kHz. Patients are arranged in groupes of 10 year intervals according to age. The bottom two graphs illustrate the expected hearing decay in healthy individuals based on ISO 7029. Left graphs for men and right graphs for women. σ = Standard deviations of all frequencies for the given age range (zPTA6). Hz = Hertz. dB HL = Decibels hearing level.
Fig 2.
Average Hearing Thresholds for Men and Women with Fabry Disease.
Mean Z-Score values of hearing levels for all Fabry patients on measured frequencies 0.25kHz-8kHz. Squares represent men and circles represent women. Confidence interval at 95%. Z-Scores indicate how many standard deviations a Fabry patients hearing threshold deviates from a sex and age corresponding healthy individual. Hz = Hertz.
Table 1.
Demographic, renal and audiometric data of Fabry disease patients.
Table 2.
Genotypes and phenotypes of the Danish Fabry disease patient population.
Table 3.
Hearing difference between men and women with Fabry disease according to frequency.