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Open Access
Peer-reviewed
Research Article
The effect of casein glycomacropeptide versus free synthetic amino acids for early treatment of phenylketonuria in a mice model
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Kirsten K. Ahring ,
Roles Conceptualization, Data curation, Formal analysis, Funding acquisition, Investigation, Methodology, Project administration, Writing – original draft
* E-mail: kirsten.kiaer.ahring@regionh.dk
Affiliation Departments of Paediatrics and Clinical Genetics, PKU Clinic, Kennedy Center, Copenhagen University Hospital, Rigshospitalet, Denmark
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Frederik Dagnæs-Hansen,
Roles Conceptualization, Investigation, Project administration, Supervision, Writing – review & editing
Affiliation Department of Biomedicine, Health, Aarhus University, Aarhus, Denmark
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Annemarie Brüel,
Roles Conceptualization, Data curation, Formal analysis, Supervision, Writing – review & editing
Affiliation Department of Biomedicine, Health, Aarhus University, Aarhus, Denmark
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Mette Christensen,
Roles Formal analysis, Methodology, Validation, Writing – review & editing
Affiliation Departments of Paediatrics and Clinical Genetics, Centre for Inherited Metabolic Diseases, Copenhagen University Hospital, Rigshospitalet, Denmark
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Erik Jensen,
Roles Conceptualization, Formal analysis, Funding acquisition, Project administration, Supervision, Writing – review & editing
Affiliation Arla Foods Ingredients Group P/S, Viby J, Denmark
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Thomas G. Jensen,
Roles Conceptualization, Resources, Writing – review & editing
Affiliation Department of Biomedicine, Health, Aarhus University, Aarhus, Denmark
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Mogens Johannsen,
Roles Data curation, Formal analysis, Methodology, Supervision, Writing – review & editing
Affiliation Department of Forensic Medicine, Aarhus University, Skejby, Aarhus, Denmark
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Karen S. Johansen,
Roles Data curation, Investigation, Supervision, Writing – review & editing
Affiliation Department of Biomedicine, Health, Aarhus University, Aarhus, Denmark
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Allan M. Lund,
Roles Project administration, Supervision, Writing – review & editing
Affiliation Departments of Paediatrics and Clinical Genetics, Centre for Inherited Metabolic Diseases, Copenhagen University Hospital, Rigshospitalet, Denmark
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Jesper G. Madsen,
Roles Investigation, Writing – review & editing
Affiliation Department of Biomedicine, Health, Aarhus University, Aarhus, Denmark
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Karen Brøndum-Nielsen,
Roles Conceptualization, Supervision, Writing – review & editing
Affiliation Departments of Paediatrics and Clinical Genetics, PKU Clinic, Kennedy Center, Copenhagen University Hospital, Rigshospitalet, Denmark
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Michael Pedersen,
Roles Conceptualization, Formal analysis, Investigation, Methodology, Supervision, Writing – review & editing
Affiliation Comparative Medicine Lab, Aarhus University Hospital, Aarhus, Denmark
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Lambert K. Sørensen,
Roles Formal analysis, Investigation, Methodology, Supervision, Validation, Writing – review & editing
Affiliation Department of Forensic Medicine, Aarhus University, Skejby, Aarhus, Denmark
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Mads Kjolby,
Roles Conceptualization, Data curation, Formal analysis, Investigation, Methodology, Software, Supervision, Writing – review & editing
Affiliations Department of Biomedicine, Health, Aarhus University, Aarhus, Denmark, Steno Diabetes Center Aarhus, Aarhus University Hospital, Aarhus, Denmark, Department of Clinical Pharmacology, Aarhus University Hospital, Aarhus, Denmark
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Lisbeth B. Møller
Roles Conceptualization, Formal analysis, Methodology, Project administration, Supervision, Writing – review & editing
Affiliation Department of Clinical Genetics, Kennedy Center, Copenhagen University Hospital, Rigshospitalet, Denmark
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The effect of casein glycomacropeptide versus free synthetic amino acids for early treatment of phenylketonuria in a mice model
- Kirsten K. Ahring,
- Frederik Dagnæs-Hansen,
- Annemarie Brüel,
- Mette Christensen,
- Erik Jensen,
- Thomas G. Jensen,
- Mogens Johannsen,
- Karen S. Johansen,
- Allan M. Lund,
- Jesper G. Madsen
- Published: January 11, 2022
- https://doi.org/10.1371/journal.pone.0261150