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Open Access
Peer-reviewed
Research Article
Dexamethasone is associated with early deaths in light chain amyloidosis patients with severe cardiac involvement
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Mélanie Bézard ,
Roles Data curation, Formal analysis, Investigation, Methodology, Writing – original draft, Writing – review & editing
* E-mail: melanie.bezard@aphp.fr
Affiliations The French Cardiac Amyloidosis Reference Center, GRC Amyloid Research Institute, Réseau amylose Mondor, and DHU A-TVB, Créteil, France, Cardiology Department, Assistance Publique des Hôpitaux de Paris, University Hospital Henri Mondor, Créteil, France
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Silvia Oghina,
Roles Conceptualization, Investigation, Writing – review & editing
Affiliations The French Cardiac Amyloidosis Reference Center, GRC Amyloid Research Institute, Réseau amylose Mondor, and DHU A-TVB, Créteil, France, Cardiology Department, Assistance Publique des Hôpitaux de Paris, University Hospital Henri Mondor, Créteil, France
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Damien Vitiello,
Roles Conceptualization, Formal analysis, Investigation, Methodology, Supervision, Validation, Writing – original draft, Writing – review & editing
Affiliations Sport and Health Sciences Institute (I3SP–EA3625), Paris University, Paris, France, Sorbonne University, Institut de Biologie Paris-Seine (IBPS), CNRS UMR 8256, Inserm ERL U1164, Adaptation biologique et vieillissement, Paris, France
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Mounira Kharoubi,
Roles Investigation, Resources, Writing – review & editing
Affiliations The French Cardiac Amyloidosis Reference Center, GRC Amyloid Research Institute, Réseau amylose Mondor, and DHU A-TVB, Créteil, France, Cardiology Department, Assistance Publique des Hôpitaux de Paris, University Hospital Henri Mondor, Créteil, France
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Ekaterini Kordeli,
Roles Conceptualization, Writing – review & editing
Affiliation Sorbonne University, Institut de Biologie Paris-Seine (IBPS), CNRS UMR 8256, Inserm ERL U1164, Adaptation biologique et vieillissement, Paris, France
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Arnault Galat,
Roles Investigation, Writing – review & editing
Affiliations The French Cardiac Amyloidosis Reference Center, GRC Amyloid Research Institute, Réseau amylose Mondor, and DHU A-TVB, Créteil, France, Cardiology Department, Assistance Publique des Hôpitaux de Paris, University Hospital Henri Mondor, Créteil, France
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Amira Zaroui,
Roles Investigation, Writing – review & editing
Affiliations The French Cardiac Amyloidosis Reference Center, GRC Amyloid Research Institute, Réseau amylose Mondor, and DHU A-TVB, Créteil, France, Cardiology Department, Assistance Publique des Hôpitaux de Paris, University Hospital Henri Mondor, Créteil, France
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Soulef Guendouz,
Roles Investigation, Writing – review & editing
Affiliations The French Cardiac Amyloidosis Reference Center, GRC Amyloid Research Institute, Réseau amylose Mondor, and DHU A-TVB, Créteil, France, Cardiology Department, Assistance Publique des Hôpitaux de Paris, University Hospital Henri Mondor, Créteil, France
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Floriane Gilles,
Roles Conceptualization, Formal analysis, Investigation, Methodology, Validation, Writing – original draft, Writing – review & editing
Affiliations The French Cardiac Amyloidosis Reference Center, GRC Amyloid Research Institute, Réseau amylose Mondor, and DHU A-TVB, Créteil, France, Cardiology Department, Assistance Publique des Hôpitaux de Paris, University Hospital Henri Mondor, Créteil, France
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Jason Shourick,
Roles Formal analysis, Methodology, Writing – review & editing
Affiliation EA 7379, EpiDermE, UPEC, Créteil, France
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David Hamon,
Roles Investigation, Writing – review & editing
Affiliation Cardiology Department, Assistance Publique des Hôpitaux de Paris, University Hospital Henri Mondor, Créteil, France
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Vincent Audard,
Roles Investigation, Writing – review & editing
Affiliation Nephrology and Transplantation Department, Rare Disease Reference Center «Syndrome Néphrotique Idiopathique», Assistance Publique des Hôpitaux de Paris, University Hospital Henri Mondor, Créteil, France
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Emmanuel Teiger,
Roles Investigation, Writing – review & editing
Affiliations The French Cardiac Amyloidosis Reference Center, GRC Amyloid Research Institute, Réseau amylose Mondor, and DHU A-TVB, Créteil, France, Cardiology Department, Assistance Publique des Hôpitaux de Paris, University Hospital Henri Mondor, Créteil, France, Université Paris Est Créteil (UPEC), Institut National de la Santé et de la Recherche Médicale (INSERM) U955, Institut Mondor de Recherche Biomédicale (IMRB), Créteil, France
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Elsa Poullot,
Roles Investigation, Writing – review & editing
Affiliations Université Paris Est Créteil (UPEC), Institut National de la Santé et de la Recherche Médicale (INSERM) U955, Institut Mondor de Recherche Biomédicale (IMRB), Créteil, France, Anatomy and Cytopathology, Assistance Publique des Hôpitaux de Paris, University Hospital Henri Mondor, Créteil, France
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Valérie Molinier-Frenkel,
Roles Investigation, Writing – review & editing
Affiliations Université Paris Est Créteil (UPEC), Institut National de la Santé et de la Recherche Médicale (INSERM) U955, Institut Mondor de Recherche Biomédicale (IMRB), Créteil, France, Immunology Laboratory, Créteil, France
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François Lemonnier,
Roles Investigation, Writing – review & editing
Affiliation Hematopathology-Lymphoid Unit, Assistance Publique des Hôpitaux de Paris, University Hospital Henri Mondor, Créteil, France
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Onnik Agbulut,
Roles Formal analysis, Investigation, Methodology, Resources, Supervision, Validation, Writing – review & editing
Affiliation Sorbonne University, Institut de Biologie Paris-Seine (IBPS), CNRS UMR 8256, Inserm ERL U1164, Adaptation biologique et vieillissement, Paris, France
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Fabien Le Bras,
Roles Investigation, Writing – review & editing
Affiliation Hematopathology-Lymphoid Unit, Assistance Publique des Hôpitaux de Paris, University Hospital Henri Mondor, Créteil, France
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Thibaud Damy
Roles Conceptualization, Formal analysis, Funding acquisition, Investigation, Methodology, Supervision, Validation, Writing – original draft, Writing – review & editing
Affiliations The French Cardiac Amyloidosis Reference Center, GRC Amyloid Research Institute, Réseau amylose Mondor, and DHU A-TVB, Créteil, France, Cardiology Department, Assistance Publique des Hôpitaux de Paris, University Hospital Henri Mondor, Créteil, France, Université Paris Est Créteil (UPEC), Institut National de la Santé et de la Recherche Médicale (INSERM) U955, Institut Mondor de Recherche Biomédicale (IMRB), Créteil, France
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Dexamethasone is associated with early deaths in light chain amyloidosis patients with severe cardiac involvement
- Mélanie Bézard,
- Silvia Oghina,
- Damien Vitiello,
- Mounira Kharoubi,
- Ekaterini Kordeli,
- Arnault Galat,
- Amira Zaroui,
- Soulef Guendouz,
- Floriane Gilles,
- Jason Shourick
- Published: September 15, 2021
- https://doi.org/10.1371/journal.pone.0257189