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Open Access
Peer-reviewed
Research Article
Clinical validation of an evidence-based method to adjust Pancreatic Enzyme Replacement Therapy through a prospective interventional study in paediatric patients with Cystic Fibrosis
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Joaquim Calvo-Lerma ,
Roles Conceptualization, Data curation, Formal analysis, Funding acquisition, Investigation, Methodology, Project administration, Resources, Supervision, Validation, Visualization, Writing – original draft, Writing – review & editing
* E-mail: joaquin_calvo@iislafe.es
Affiliations Instituto de Investigación Sanitaria La Fe de Valencia, Valencia, Spain, Universitat Politècnica de València, Research Institute of Food Engineering for Development, Valencia, Spain
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Jessie Hulst,
Roles Data curation, Formal analysis, Investigation, Methodology, Supervision, Validation, Writing – original draft, Writing – review & editing
Affiliation Erasmus Medical Center, Sophia Children’s Hospital, GD Rotterdam, the Netherlands
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Mieke Boon,
Roles Data curation, Formal analysis, Investigation, Methodology, Supervision, Validation, Writing – original draft, Writing – review & editing
Affiliation Pediatric Pulmonology and Cystic Fibrosis Unit, Department of Pediatrics, University Hospitals Leuven, Leuven, Belgium
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Carla Colombo,
Roles Conceptualization, Resources, Supervision, Validation, Visualization, Writing – original draft, Writing – review & editing
Affiliation CF Center, Università degli Studi di Milano, Fondazione IRCCS Ca’ Granda, Ospedale Maggiore Policlinico, Via Commenda 9, Milan, Italy
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Etna Masip,
Roles Data curation, Formal analysis, Investigation, Methodology, Writing – original draft
Affiliation Instituto de Investigación Sanitaria La Fe de Valencia, Valencia, Spain
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Mar Ruperto,
Roles Data curation, Formal analysis, Investigation, Methodology, Writing – original draft, Writing – review & editing
Affiliation Hospital Universitario Ramón y Cajal, Carretera Colmenar Viejo km 9, Madrid, Spain
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Victoria Fornés-Ferrer,
Roles Conceptualization, Data curation, Formal analysis, Methodology, Software, Validation, Visualization, Writing – original draft, Writing – review & editing
Affiliation Instituto de Investigación Sanitaria La Fe de Valencia, Valencia, Spain
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Els van der Wiel,
Roles Data curation, Formal analysis, Investigation, Methodology, Writing – review & editing
Affiliation Erasmus Medical Center, Sophia Children’s Hospital, GD Rotterdam, the Netherlands
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Ine Claes,
Roles Data curation, Investigation, Methodology, Project administration, Writing – review & editing
Affiliation Pediatric Pulmonology and Cystic Fibrosis Unit, Department of Pediatrics, University Hospitals Leuven, Leuven, Belgium
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Maria Garriga,
Roles Data curation, Investigation, Methodology, Project administration, Writing – review & editing
Affiliation Hospital Universitario Ramón y Cajal, Carretera Colmenar Viejo km 9, Madrid, Spain
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Maria Roca,
Roles Data curation, Formal analysis, Investigation, Methodology, Writing – review & editing
Affiliation Instituto de Investigación Sanitaria La Fe de Valencia, Valencia, Spain
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Paula Crespo-Escobar,
Roles Data curation, Formal analysis, Investigation, Methodology, Project administration, Writing – review & editing
Affiliation Instituto de Investigación Sanitaria La Fe de Valencia, Valencia, Spain
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Anna Bulfamante,
Roles Data curation, Investigation, Methodology, Writing – review & editing
Affiliation CF Center, Università degli Studi di Milano, Fondazione IRCCS Ca’ Granda, Ospedale Maggiore Policlinico, Via Commenda 9, Milan, Italy
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Sandra Woodcock,
Roles Conceptualization, Data curation, Formal analysis, Investigation, Methodology, Project administration, Writing – review & editing
Affiliation Erasmus Medical Center, Sophia Children’s Hospital, GD Rotterdam, the Netherlands
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Sandra Martínez-Barona,
Roles Data curation, Investigation, Methodology, Writing – review & editing
Affiliation Instituto de Investigación Sanitaria La Fe de Valencia, Valencia, Spain
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Ana Andrés,
Roles Conceptualization, Data curation, Formal analysis, Funding acquisition, Investigation, Methodology, Project administration, Resources, Supervision, Validation, Visualization, Writing – original draft, Writing – review & editing
Affiliation Universitat Politècnica de València, Research Institute of Food Engineering for Development, Valencia, Spain
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Kris de Boeck,
Roles Data curation, Formal analysis, Funding acquisition, Investigation, Methodology, Project administration, Resources, Supervision, Validation, Visualization, Writing – original draft, Writing – review & editing
Affiliation Pediatric Pulmonology and Cystic Fibrosis Unit, Department of Pediatrics, University Hospitals Leuven, Leuven, Belgium
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Carmen Ribes-Koninckx,
Roles Conceptualization, Data curation, Formal analysis, Funding acquisition, Investigation, Methodology, Project administration, Resources, Supervision, Validation, Visualization, Writing – original draft, Writing – review & editing
Affiliation Instituto de Investigación Sanitaria La Fe de Valencia, Valencia, Spain
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on behalf of MyCyFAPP project
¶The complete membership of the author group can be found in the Acknowledgments.
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Clinical validation of an evidence-based method to adjust Pancreatic Enzyme Replacement Therapy through a prospective interventional study in paediatric patients with Cystic Fibrosis
- Joaquim Calvo-Lerma,
- Jessie Hulst,
- Mieke Boon,
- Carla Colombo,
- Etna Masip,
- Mar Ruperto,
- Victoria Fornés-Ferrer,
- Els van der Wiel,
- Ine Claes,
- Maria Garriga
- Published: March 12, 2019
- https://doi.org/10.1371/journal.pone.0213216