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Open Access
Peer-reviewed
Research Article
Characterization of Defects in Ion Transport and Tissue Development in Cystic Fibrosis Transmembrane Conductance Regulator (CFTR)-Knockout Rats
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Katherine L. Tuggle,
Affiliations Gregory Fleming James Cystic Fibrosis Research Center, University of Alabama at Birmingham, Birmingham, Alabama, United States of America, Department of Environmental Health Sciences, School of Public Health, University of Alabama at Birmingham, Birmingham, Alabama, United States of America
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Susan E. Birket,
Affiliations Gregory Fleming James Cystic Fibrosis Research Center, University of Alabama at Birmingham, Birmingham, Alabama, United States of America, Department of Medicine, University of Alabama at Birmingham, Birmingham, Alabama, United States of America
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Xiaoxia Cui,
Affiliation SAGE Labs, Inc., St. Louis, Missouri, United States of America
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Jeong Hong,
Affiliations Gregory Fleming James Cystic Fibrosis Research Center, University of Alabama at Birmingham, Birmingham, Alabama, United States of America, Department of Cell, Developmental, and Integrative Biology, University of Alabama at Birmingham, Birmingham, Alabama, United States of America
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Joe Warren,
Affiliation SAGE Labs, Inc., St. Louis, Missouri, United States of America
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Lara Reid,
Affiliation SAGE Labs, Inc., St. Louis, Missouri, United States of America
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Andre Chambers,
Affiliation SAGE Labs, Inc., St. Louis, Missouri, United States of America
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Diana Ji,
Affiliation SAGE Labs, Inc., St. Louis, Missouri, United States of America
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Kevin Gamber,
Affiliation SAGE Labs, Inc., St. Louis, Missouri, United States of America
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Kengyeh K. Chu,
Affiliations Wellman Center for Photomedicine, Harvard Medical School, Massachusetts General Hospital, Boston, Massachusetts, United States of America, Department of Dermatology, Massachusetts General Hospital, Boston, Massachusetts, United States of America
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Guillermo Tearney,
Affiliations Wellman Center for Photomedicine, Harvard Medical School, Massachusetts General Hospital, Boston, Massachusetts, United States of America, Department of Pathology, Massachusetts General Hospital, Boston, Massachusetts, United States of America
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Li Ping Tang,
Affiliation Gregory Fleming James Cystic Fibrosis Research Center, University of Alabama at Birmingham, Birmingham, Alabama, United States of America
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James A. Fortenberry,
Affiliation Gregory Fleming James Cystic Fibrosis Research Center, University of Alabama at Birmingham, Birmingham, Alabama, United States of America
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Ming Du,
Affiliations Gregory Fleming James Cystic Fibrosis Research Center, University of Alabama at Birmingham, Birmingham, Alabama, United States of America, Animal Resources Program, Office of the Vice President for Research, University of Alabama at Birmingham, Birmingham, Alabama, United States of America
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Joan M. Cadillac,
Affiliation Animal Resources Program, Office of the Vice President for Research, University of Alabama at Birmingham, Birmingham, Alabama, United States of America
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David M. Bedwell,
Affiliations Gregory Fleming James Cystic Fibrosis Research Center, University of Alabama at Birmingham, Birmingham, Alabama, United States of America, Department of Microbiology, University of Alabama at Birmingham, Birmingham, Alabama, United States of America
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Steven M. Rowe,
Affiliations Gregory Fleming James Cystic Fibrosis Research Center, University of Alabama at Birmingham, Birmingham, Alabama, United States of America, Department of Medicine, University of Alabama at Birmingham, Birmingham, Alabama, United States of America
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Eric J. Sorscher,
Affiliations Gregory Fleming James Cystic Fibrosis Research Center, University of Alabama at Birmingham, Birmingham, Alabama, United States of America, Department of Medicine, University of Alabama at Birmingham, Birmingham, Alabama, United States of America
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Michelle V. Fanucchi
* E-mail: fanucchi@uab.edu
Affiliations Gregory Fleming James Cystic Fibrosis Research Center, University of Alabama at Birmingham, Birmingham, Alabama, United States of America, Department of Environmental Health Sciences, School of Public Health, University of Alabama at Birmingham, Birmingham, Alabama, United States of America
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Characterization of Defects in Ion Transport and Tissue Development in Cystic Fibrosis Transmembrane Conductance Regulator (CFTR)-Knockout Rats
- Katherine L. Tuggle,
- Susan E. Birket,
- Xiaoxia Cui,
- Jeong Hong,
- Joe Warren,
- Lara Reid,
- Andre Chambers,
- Diana Ji,
- Kevin Gamber,
- Kengyeh K. Chu
- Published: March 7, 2014
- https://doi.org/10.1371/journal.pone.0091253