Omigapil Treatment Decreases Fibrosis and Improves Respiratory Rate in dy2J Mouse Model of Congenital Muscular Dystrophy

Qing Yu; Arpana Sali; Jack Van der Meulen; Brittany K. Creeden; Heather Gordish-Dressman; Anne Rutkowski; Sree Rayavarapu; Kitipong Uaesoontrachoon; Tony Huynh; Kanneboyina Nagaraju; Christopher F. Spurney

doi:10.1371/journal.pone.0065468

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Open Access

Peer-reviewed

Research Article

Omigapil Treatment Decreases Fibrosis and Improves Respiratory Rate in dy^2J Mouse Model of Congenital Muscular Dystrophy

Qing Yu,

Affiliation Center for Genetic Medicine Research, Children’s National Medical Center, Washington DC, United States of America
⨯
Arpana Sali,

Affiliation Center for Genetic Medicine Research, Children’s National Medical Center, Washington DC, United States of America
⨯
Jack Van der Meulen,

Affiliation Center for Genetic Medicine Research, Children’s National Medical Center, Washington DC, United States of America
⨯
Brittany K. Creeden,

Affiliation Center for Genetic Medicine Research, Children’s National Medical Center, Washington DC, United States of America
⨯
Heather Gordish-Dressman,

Affiliation Center for Genetic Medicine Research, Children’s National Medical Center, Washington DC, United States of America
⨯
Anne Rutkowski,

Affiliation Kaiser SCPMG, Cure CMD, Olathe, Kansas, United States of America
⨯
Sree Rayavarapu,

Affiliation Center for Genetic Medicine Research, Children’s National Medical Center, Washington DC, United States of America
⨯
Kitipong Uaesoontrachoon,

Affiliation Center for Genetic Medicine Research, Children’s National Medical Center, Washington DC, United States of America
⨯
Tony Huynh,

Affiliation Center for Genetic Medicine Research, Children’s National Medical Center, Washington DC, United States of America
⨯
Kanneboyina Nagaraju,

Affiliation Center for Genetic Medicine Research, Children’s National Medical Center, Washington DC, United States of America
⨯
Christopher F. Spurney

* E-mail: cspurney@childrensnational.org

Affiliations Center for Genetic Medicine Research, Children’s National Medical Center, Washington DC, United States of America, Division of Cardiology, Children’s National Medical Center, Washington DC, United States of America
⨯

Omigapil Treatment Decreases Fibrosis and Improves Respiratory Rate in dy^2J Mouse Model of Congenital Muscular Dystrophy

Qing Yu,
Arpana Sali,
Jack Van der Meulen,
Brittany K. Creeden,
Heather Gordish-Dressman,
Anne Rutkowski,
Sree Rayavarapu,
Kitipong Uaesoontrachoon,
Tony Huynh,
Kanneboyina Nagaraju

Published: June 6, 2013
https://doi.org/10.1371/journal.pone.0065468

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