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Open Access
Peer-reviewed
Research Article
Compromised Mitochondrial Fatty Acid Synthesis in Transgenic Mice Results in Defective Protein Lipoylation and Energy Disequilibrium
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Stuart Smith ,
* E-mail: ssmith@chori.org
Affiliation Children's Hospital Oakland Research Institute, Oakland, California, United States of America
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Andrzej Witkowski,
Affiliation Children's Hospital Oakland Research Institute, Oakland, California, United States of America
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Ayesha Moghul,
Affiliation Children's Hospital Oakland Research Institute, Oakland, California, United States of America
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Yuko Yoshinaga,
Affiliation Children's Hospital Oakland Research Institute, Oakland, California, United States of America
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Michael Nefedov,
Affiliation Children's Hospital Oakland Research Institute, Oakland, California, United States of America
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Pieter de Jong,
Affiliation Children's Hospital Oakland Research Institute, Oakland, California, United States of America
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Dejiang Feng,
Affiliation Children's Hospital Oakland Research Institute, Oakland, California, United States of America
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Loren Fong,
Affiliation Department of Medicine, University of California Los Angeles, Los Angeles, California, United States of America
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Yiping Tu,
Affiliation Department of Medicine, University of California Los Angeles, Los Angeles, California, United States of America
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Yan Hu,
Affiliation Department of Medicine, University of California Los Angeles, Los Angeles, California, United States of America
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Stephen G. Young,
Affiliation Department of Medicine, University of California Los Angeles, Los Angeles, California, United States of America
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Thomas Pham,
Affiliation Children's Hospital Oakland Research Institute, Oakland, California, United States of America
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Carling Cheung,
Affiliation Children's Hospital Oakland Research Institute, Oakland, California, United States of America
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Shana M. Katzman,
Affiliation Buck Institute for Research on Aging, Novato, California, United States of America
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Martin D. Brand,
Affiliation Buck Institute for Research on Aging, Novato, California, United States of America
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Casey L. Quinlan,
Affiliation Buck Institute for Research on Aging, Novato, California, United States of America
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Marcel Fens,
Affiliation Children's Hospital Oakland Research Institute, Oakland, California, United States of America
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Frans Kuypers,
Affiliation Children's Hospital Oakland Research Institute, Oakland, California, United States of America
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Stephanie Misquitta,
Affiliation Children's Hospital Oakland Research Institute, Oakland, California, United States of America
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Stephen M. Griffey,
Affiliation School of Veterinary Medicine, University of California Davis, Davis, California, United States of America
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Son Tran,
Affiliation Children's Hospital Oakland Research Institute, Oakland, California, United States of America
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Afshin Gharib,
Affiliations Children's Hospital Oakland Research Institute, Oakland, California, United States of America, Dominican University of California, San Rafael, California, United States of America
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Jens Knudsen,
Affiliation Department of Biochemistry and Molecular Biology, Odense University, Odense, Denmark
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Hans Kristian Hannibal-Bach,
Affiliation Department of Biochemistry and Molecular Biology, Odense University, Odense, Denmark
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Grace Wang,
Affiliation Children's Hospital Oakland Research Institute, Oakland, California, United States of America
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Sandra Larkin,
Affiliation Children's Hospital Oakland Research Institute, Oakland, California, United States of America
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Jennifer Thweatt,
Affiliation Children's Hospital Oakland Research Institute, Oakland, California, United States of America
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Saloni Pasta
Affiliation Children's Hospital Oakland Research Institute, Oakland, California, United States of America
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Compromised Mitochondrial Fatty Acid Synthesis in Transgenic Mice Results in Defective Protein Lipoylation and Energy Disequilibrium
- Stuart Smith,
- Andrzej Witkowski,
- Ayesha Moghul,
- Yuko Yoshinaga,
- Michael Nefedov,
- Pieter de Jong,
- Dejiang Feng,
- Loren Fong,
- Yiping Tu,
- Yan Hu
- Published: October 15, 2012
- https://doi.org/10.1371/journal.pone.0047196