Metabolite Profiles Reveal Energy Failure and Impaired Beta-Oxidation in Liver of Mice with Complex III Deficiency Due to a BCS1L Mutation

• Heike Kotarsky,

  Affiliation Department of Pediatrics, Clinical Sciences, Lund University, Lund, Sweden

  ⨯
• Matthias Keller,

  Affiliation Neonatology, Department of Pediatrics, University Hospital, Essen, Germany

  ⨯
• Mina Davoudi,

  Affiliation Department of Pediatrics, Clinical Sciences, Lund University, Lund, Sweden

  ⨯
• Per Levéen,

  Affiliation Department of Pediatrics, Clinical Sciences, Lund University, Lund, Sweden

  ⨯
• Riitta Karikoski,

  Affiliation Central Pathology Laboratory, Helsinki University Hospital Laboratory Diagnostics, Helsinki, Finland

  ⨯
• David P. Enot,

  Affiliation Neonatology, Department of Pediatrics, University Hospital, Essen, Germany

  ⨯
• Vineta Fellman

  * E-mail: Vineta.Fellman@med.lu.se

  Affiliations Department of Pediatrics, Clinical Sciences, Lund University, Lund, Sweden, Children’s Hospital, Helsinki University Hospital and University of Helsinki, Helsinki, Finland, Folkhälsan Research Center, Helsinki, Finland

  ⨯