Treatment of CoQ₁₀ Deficient Fibroblasts with Ubiquinone, CoQ Analogs, and Vitamin C: Time- and Compound-Dependent Effects

• Luis C. López ,

  Contributed equally to this work with: Luis C. López, Catarina M. Quinzii

  Affiliation Department of Neurology, Columbia University Medical Center, New York, New York, United States of America

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• Catarina M. Quinzii ,

  Contributed equally to this work with: Luis C. López, Catarina M. Quinzii

  Affiliation Department of Neurology, Columbia University Medical Center, New York, New York, United States of America

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• Estela Area,

  Affiliation Department of Neurology, Columbia University Medical Center, New York, New York, United States of America

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• Ali Naini,

  Affiliation Department of Neurology, Columbia University Medical Center, New York, New York, United States of America

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• Shamima Rahman,

  Affiliation Clinical and Molecular Genetics Unit, University College London Institute of Child Health, London, United Kingdom

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• Markus Schuelke,

  Affiliation Department of Neuropediatrics, Charité Virchow University Hospital, Berlin, Germany

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• Leonardo Salviati,

  Affiliation Servizio di Genetica Clinica ed Epidemiologica, Department of Pediatrics, University of Padova, Padova, Italy

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• Salvatore DiMauro,

  Affiliation Department of Neurology, Columbia University Medical Center, New York, New York, United States of America

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• Michio Hirano

  * E-mail: mh29@columbia.edu

  Affiliation Department of Neurology, Columbia University Medical Center, New York, New York, United States of America

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