About the Authors

Heledd H. Jarosz-Griffiths

Roles Conceptualization, Data curation, Formal analysis, Funding acquisition, Investigation, Methodology, Project administration, Resources, Writing – original draft, Writing – review & editing

D.G.Peckham@leeds.ac.uk (DP); H.H.Griffiths@leeds.ac.uk (HHJG)

Affiliation Leeds Institute of Medical Research, University of Leeds, Leeds, United Kingdom

Lindsey Gillgrass

Roles Data curation, Investigation, Writing – review & editing

Affiliation Adult Cystic Fibrosis Unit, St James’s University Hospital, Leeds, United Kingdom

Laura R. Caley

Roles Investigation, Writing – original draft, Writing – review & editing

Affiliation Leeds Institute of Medical Research, University of Leeds, Leeds, United Kingdom

Giulia Spoletini

Roles Investigation, Writing – review & editing

Affiliations Leeds Institute of Medical Research, University of Leeds, Leeds, United Kingdom, Adult Cystic Fibrosis Unit, St James’s University Hospital, Leeds, United Kingdom

Ian J. Clifton

Roles Funding acquisition, Investigation, Writing – review & editing

Affiliation Adult Cystic Fibrosis Unit, St James’s University Hospital, Leeds, United Kingdom

Christine Etherington

Roles Investigation, Writing – review & editing

Affiliation Adult Cystic Fibrosis Unit, St James’s University Hospital, Leeds, United Kingdom

Sinisa Savic

Roles Funding acquisition, Investigation, Methodology, Writing – review & editing

Affiliation Leeds Institute of Rheumatic and Musculoskeletal Medicine, University of Leeds, Leeds, United Kingdom

Michael F. McDermott

Roles Funding acquisition, Investigation, Methodology, Writing – original draft, Writing – review & editing

Affiliation Leeds Institute of Rheumatic and Musculoskeletal Medicine, University of Leeds, Leeds, United Kingdom

Daniel Peckham

Roles Conceptualization, Data curation, Funding acquisition, Investigation, Methodology, Project administration, Resources, Supervision, Writing – original draft, Writing – review & editing

D.G.Peckham@leeds.ac.uk (DP); H.H.Griffiths@leeds.ac.uk (HHJG)

Affiliations Leeds Institute of Medical Research, University of Leeds, Leeds, United Kingdom, Adult Cystic Fibrosis Unit, St James’s University Hospital, Leeds, United Kingdom

Competing Interests

Conflict of Interest DP: speaker/board honoraria from Vertex This does not alter our adherence to PLOS ONE policies on sharing data and materials.