About the Authors

Youcai Tang

Roles Conceptualization, Formal analysis, Methodology, Validation, Visualization, Writing – original draft, Writing – review & editing

Affiliations Pediatrics and Biochemistry, Saint Louis University, and Cardinal Glennon Children’s Medical Center, St. Louis, Missouri, United States of America, Pediatrics and Science & Education, the Fifth Affiliated Hospital, Zhengzhou University, Zhengzhou, China

Keith S. Blomenkamp

Roles Data curation, Formal analysis, Methodology, Resources, Validation, Writing – review & editing

Affiliation Pediatrics and Biochemistry, Saint Louis University, and Cardinal Glennon Children’s Medical Center, St. Louis, Missouri, United States of America

Peter Fickert

Roles Resources, Writing – review & editing

Affiliation Research Unit for Experimental and Molecular Hepatology, Division of Gastroenterology and Hepatology, Department of Internal Medicine, Medical University of Graz, Graz, Austria

Michael Trauner

Roles Resources, Writing – review & editing

Affiliation Division of Gastroenterology and Hepatology, Department of Internal Medicine III, Medical University of Vienna, Vienna, Austria

Jeffrey H. Teckman

Roles Conceptualization, Funding acquisition, Investigation, Methodology, Project administration, Resources, Supervision, Writing – review & editing

teckmanj@slu.edu

Affiliation Pediatrics and Biochemistry, Saint Louis University, and Cardinal Glennon Children’s Medical Center, St. Louis, Missouri, United States of America

Competing Interests

There are no conflicts of interest to declare. However, it is important to disclose that this research involves the use of nor-ursodeoxycholic acid which is protected under patent name “The use of nor-ursodeoxycholic acid” and number DK2392337T3. This does not alter our adherence to PLOS ONE policies on sharing data and materials.