About the Authors

Graham L. Hall

grahamh@ichr.uwa.edu.au

Affiliations Respiratory Medicine, Princess Margaret Hospital for Children, Perth, Australia, School of Paediatrics and Child Health, University of Western Australia, Perth, Australia, Telethon Institute for Child Health Research and Centre for Child Health Research, University of Western Australia, Perth, Australia

Karla M. Logie

Affiliations School of Paediatrics and Child Health, University of Western Australia, Perth, Australia, Telethon Institute for Child Health Research and Centre for Child Health Research, University of Western Australia, Perth, Australia

Faith Parsons

Affiliation Telethon Institute for Child Health Research and Centre for Child Health Research, University of Western Australia, Perth, Australia

Sven M. Schulzke

Affiliations School of Women's and Infant's Health, University of Western Australia, Perth, Australia, University Children's Hospital Basel, Basel, Switzerland

Gary Nolan

Affiliations Respiratory Medicine, Princess Margaret Hospital for Children, Perth, Australia, Telethon Institute for Child Health Research and Centre for Child Health Research, University of Western Australia, Perth, Australia

Conor Murray

Affiliation Diagnostic Imaging, Princess Margaret Hospital for Children, Perth, Australia

Sarath Ranganathan

Affiliations Respiratory Medicine, Royal Children's Hospital, Melbourne, Australia, Murdoch Children's Research Institute, Melbourne, Australia, Department of Paediatrics, University of Melbourne, Australia

Phil Robinson

Affiliations Respiratory Medicine, Royal Children's Hospital, Melbourne, Australia, Murdoch Children's Research Institute, Melbourne, Australia, Department of Paediatrics, University of Melbourne, Australia

Peter D. Sly

Affiliations Respiratory Medicine, Princess Margaret Hospital for Children, Perth, Australia, Telethon Institute for Child Health Research and Centre for Child Health Research, University of Western Australia, Perth, Australia, Queensland Children's Medical Research Institute, University of Queensland, Brisbane, Australia

Stephen M. Stick

Affiliations Respiratory Medicine, Princess Margaret Hospital for Children, Perth, Australia, School of Paediatrics and Child Health, University of Western Australia, Perth, Australia, Telethon Institute for Child Health Research and Centre for Child Health Research, University of Western Australia, Perth, Australia

on behalf of AREST CF

Affiliations Respiratory Medicine, Princess Margaret Hospital for Children, Perth, Australia, Telethon Institute for Child Health Research and Centre for Child Health Research, University of Western Australia, Perth, Australia, Respiratory Medicine, Royal Children's Hospital, Melbourne, Australia, Murdoch Children's Research Institute, Melbourne, Australia

Competing Interests

The authors have declared that no competing interests exist.

Author Contributions

Conceived and designed the experiments: GLH SR PR PDS SMS. Performed the experiments: KL GN . Analyzed the data: GLH KL FP SS CM. Wrote first and subsequent drafts: GLH. Contributed to the final draft and approved its submission: GLH KL FP SMS GN CM SR PR PDS SMS.