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Open Access
Peer-reviewed
Research Article
Short-term succinic acid treatment mitigates cerebellar mitochondrial OXPHOS dysfunction, neurodegeneration and ataxia in a Purkinje-specific spinocerebellar ataxia type 1 (SCA1) mouse model
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Austin Ferro,
Roles Data curation, Formal analysis, Methodology, Writing – review & editing
Current address: Institute for Translational Neuroscience, University of Minnesota, Minneapolis, Minnesota, United States of America
Affiliation Neuroscience Program, Skidmore College, Saratoga Springs, New York, United States of America
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Emily Carbone,
Roles Data curation, Methodology
Affiliation Neuroscience Program, Skidmore College, Saratoga Springs, New York, United States of America
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Jenny Zhang,
Roles Data curation, Methodology
Affiliation Neuroscience Program, Skidmore College, Saratoga Springs, New York, United States of America
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Evan Marzouk,
Roles Data curation, Methodology
Affiliation Neuroscience Program, Skidmore College, Saratoga Springs, New York, United States of America
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Monica Villegas,
Roles Data curation
Affiliation Neuroscience Program, Skidmore College, Saratoga Springs, New York, United States of America
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Asher Siegel,
Roles Data curation, Methodology
Affiliation Chemistry Department, Skidmore College, Saratoga Springs, New York, United States of America
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Donna Nguyen,
Roles Data curation
Affiliation Neuroscience Program, Skidmore College, Saratoga Springs, New York, United States of America
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Thomas Possidente,
Roles Data curation, Methodology
Affiliation Neuroscience Program, Skidmore College, Saratoga Springs, New York, United States of America
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Jessilyn Hartman,
Roles Data curation
Affiliation Neuroscience Program, Skidmore College, Saratoga Springs, New York, United States of America
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Kailen Polley,
Roles Data curation
Affiliation Neuroscience Program, Skidmore College, Saratoga Springs, New York, United States of America
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Melissa A. Ingram,
Roles Data curation, Formal analysis, Methodology, Validation
Affiliation Institute for Translational Neuroscience, Department of Lab Medicine and Pathology, University of Minnesota, Minneapolis, Minnesota, United States of America
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Georgia Berry,
Roles Data curation
Affiliation Neuroscience Program, Skidmore College, Saratoga Springs, New York, United States of America
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Thomas H. Reynolds,
Roles Methodology, Resources, Validation, Writing – review & editing
Affiliation Health and Exercise Science Department, Skidmore College, Saratoga Springs, New York, United States of America
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Bernard Possidente,
Roles Conceptualization, Data curation, Formal analysis, Methodology, Resources, Supervision, Writing – review & editing
Affiliations Neuroscience Program, Skidmore College, Saratoga Springs, New York, United States of America, Biology Department, Skidmore College, Saratoga Springs, New York, United States of America
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Kimberley Frederick,
Roles Conceptualization, Data curation, Formal analysis, Methodology, Resources, Supervision, Validation, Writing – review & editing
Affiliation Chemistry Department, Skidmore College, Saratoga Springs, New York, United States of America
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Stephen Ives,
Roles Conceptualization, Formal analysis, Methodology, Resources, Validation, Writing – review & editing
Affiliation Health and Exercise Science Department, Skidmore College, Saratoga Springs, New York, United States of America
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Sarita Lagalwar
Roles Conceptualization, Data curation, Formal analysis, Funding acquisition, Investigation, Methodology, Resources, Validation, Visualization, Writing – original draft, Writing – review & editing
* E-mail: slagalwa@skidmore.edu
Affiliation Neuroscience Program, Skidmore College, Saratoga Springs, New York, United States of America
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Short-term succinic acid treatment mitigates cerebellar mitochondrial OXPHOS dysfunction, neurodegeneration and ataxia in a Purkinje-specific spinocerebellar ataxia type 1 (SCA1) mouse model
- Austin Ferro,
- Emily Carbone,
- Jenny Zhang,
- Evan Marzouk,
- Monica Villegas,
- Asher Siegel,
- Donna Nguyen,
- Thomas Possidente,
- Jessilyn Hartman,
- Kailen Polley
- Published: December 6, 2017
- https://doi.org/10.1371/journal.pone.0188425