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Fig 1.

Study protocol.

Flow chart with inclusion criteria from catheter and echocardiography databases, identification of individual patients, and exclusion due to loss of clinical follow-up. Abbreviation: RHC right heart catheterization.

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Table 1.

Clinical characteristics of the study population.

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Table 2.

Hemodynamic characteristics of the study population.

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Fig 2.

Survival of patients with or without PH as diagnosed by RHC visualized by Kaplan-Meier curves.

Abbreviations: PH pulmonary hypertension, RHC right heart catheterization, mPAP mean pulmonary arterial pressure, HR hazard ratio, 95%CI 95% confidence interval.

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Fig 3.

Survival of patients with or without PH as suggested by Doppler echocardiography visualized by Kaplan-Meier curves.

Abbreviations: PH pulmonary hypertension, sPAP systolic pulmonary arterial pressure, HR hazard ratio, 95%CI 95% confidence interval.

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Fig 4.

Outcome differentiated by PAP for subgroup of patients: left ventricular cardiomyopathy (CMP):A,B; valvular heart disease: C,D; ischemic heart disease (IHD): E,F and rare cardiac diseases: G;H. Invasive measurements by RHC (A,C,E,G) are compared to non-invasively assessment by DE (B,D,F,G). Abbreviations: m/sPAP mean/systolic pulmonary arterial pressure, HR hazard ratio, 95%CI 95% confidence interval, ns not significant.

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Fig 5.

Kaplan-Meier curves for survival of patients with PH due to LHD or precapillary PH defined by RHC according to mPAP and PCWP (A) or elevated PVR (≥ 250 dynxsxcm-5 or 3.1 WU, B). Abbreviations: PH pulmonary hypertension, LHD left heart disease, RHC right heart catheterization, PAP pulmonary arterial pressure, mPAP mean pulmonary arterial pressure, PVR pulmonary vascular resistance, WU Wood Units, HR hazard ratio, 95%CI 95% confidence interval, ns not significant.

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Table 3.

Univariate survival analysis by Cox proportional regression.

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Table 4.

Multivariate analysis for independent predictive parameters.

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Fig 6.

Incremental predictive information for survival of multimodal clinical settings based on complete-case data (n = 395).

Abbreviations: Clin: clinical assessment (age, sex, NYHA functional class), Clin+Echo: clinical assessment and transthoracic (Doppler) echocardiography (LV-EF, RV dysfunction, sPAP, RAP), Clin+Sero: clinical assessment and cardiac serological parameters (NT-proBNP, cTnT); Clin+Sero+Echo: clinical assessment, cardiac serological parameters and transthoracic echocardiography combined; Clin+Sero+Echo+RHC: Non-invasive diagnostics and RHC (CI, mPAP, RAP) combined; Clin+RHC: clinical assessment and RHC (CI, mPAP, RAP) combined. **p<0.001. NYHA New York Heart Association, LV-EF left ventricular ejection fraction, sPAP systolic pulmonary arterial pressure, RAP right atrial pressure, NT-proBNP N-terminal pro brain natriuretic peptide, cTnT cardiac troponin T, CI cardiac index, mPAP mean pulmonary arterial pressure, RHC right heart catheterization.

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