About the Authors

Wesley R. Lewis

Affiliation Department of Cell, Developmental and Integrative Biology, University of Alabama at Birmingham, Birmingham, Alabama, United States of America

Erik B. Malarkey

Affiliation Department of Cell, Developmental and Integrative Biology, University of Alabama at Birmingham, Birmingham, Alabama, United States of America

Douglas Tritschler

Affiliation Genetics, Cell Biology, and Development, University of Minnesota Medical School, Minneapolis, Minnesota, United States of America

Raqual Bower

Affiliation Genetics, Cell Biology, and Development, University of Minnesota Medical School, Minneapolis, Minnesota, United States of America

Raymond C. Pasek

Affiliation Cell and Developmental Biology, Vanderbilt University, Nashville, Tennessee, United States of America

Jonathan D. Porath

Affiliation Division of Nephrology, Department of Medicine, Boston Children’s Hospital, Harvard Medical School, Boston, Massachusetts, United States of America

Susan E. Birket

Affiliations Department of Medicine, University of Alabama at Birmingham, Birmingham, Alabama, United States of America, Cystic Fibrosis Research Center, University of Alabama at Birmingham, Birmingham, Alabama, United States of America

Sophie Saunier

Affiliations INSERM, U-983, Necker Hospital, Paris, France, Paris Descartes University, Sorbonne Paris Cité, Imagine Institute, Paris, France

Corinne Antignac

Affiliations Institut National de la Santé et de la Recherche Médicale (INSERM) Unité Mixte de Recherche (UMR) 1163, Laboratory of Hereditary Kidney Diseases, Paris, France, Assistance Publique-Hôpitaux de Paris, Department of Genetics, Necker Hospital, Paris, France

Michael R. Knowles

Affiliation Department of Medicine, UNC School of Medicine, Marisco Lung Institute, Chapel Hill, North Carolina, United States of America

Margaret W. Leigh

Affiliation Department of Pediatrics, UNC School of Medicine, Marisco Lung Institute, Chapel Hill, North Carolina, United States of America

Maimoona A. Zariwala

Affiliation Department of Pathology and Laboratory Medicine, UNC School of Medicine, Marisco Lung Institute, Chapel Hill, North Carolina, United States of America

Anil K. Challa

Affiliation Department of Genetics, University of Alabama at Birmingham, Birmingham, Alabama, United States of America

Robert A. Kesterson

Affiliation Department of Genetics, University of Alabama at Birmingham, Birmingham, Alabama, United States of America

Steven M. Rowe

Affiliations Department of Medicine, University of Alabama at Birmingham, Birmingham, Alabama, United States of America, Cystic Fibrosis Research Center, University of Alabama at Birmingham, Birmingham, Alabama, United States of America

Iain A. Drummond

Affiliation Nephrology Division, Massachusetts General Hospital, Charlestown, Massachusetts, United States of America

John M. Parant

Affiliation Department of Pharmacology and Toxicology, University of Alabama at Birmingham, Birmingham, Alabama, United States of America

Friedhelm Hildebrandt

Affiliation Division of Nephrology, Department of Medicine, Boston Children’s Hospital, Harvard Medical School, Boston, Massachusetts, United States of America

Mary E. Porter

Affiliation Genetics, Cell Biology, and Development, University of Minnesota Medical School, Minneapolis, Minnesota, United States of America

Bradley K. Yoder

byoder@uab.edu (BKY); nberbari@iupui.edu (NFB)

Affiliation Department of Cell, Developmental and Integrative Biology, University of Alabama at Birmingham, Birmingham, Alabama, United States of America

Nicolas F. Berbari

byoder@uab.edu (BKY); nberbari@iupui.edu (NFB)

Affiliation Department of Biology, Indiana University-Purdue University Indianapolis, Indianapolis, Indiana, United States of America

Competing Interests

The authors have declared that no competing interests exist.

Author Contributions

Conceived and designed the experiments: WRL EBM DT BKY NFB. Performed the experiments: WRL EBM DT RB RCP JDP SEB SS CA MRK MAZ AKC MEP NFB. Analyzed the data: WRL EBM DT RB RCP SEB SS CA MAZ AKC RAK SMR IAD JMP FH MEP BKY NFB. Contributed reagents/materials/analysis tools: AKC RAK SMR IAD FH MEP BKY. Wrote the paper: WRL EBM AKC JMP FH MEP BKY NFB.