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Open Access
Peer-reviewed
Research Article
Neuron-specific ablation of the Krabbe disease gene galactosylceramidase in mice results in neurodegeneration
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Conlan Kreher ,
Contributed equally to this work with: Conlan Kreher, Jacob Favret
Roles Conceptualization, Formal analysis, Investigation, Methodology, Software, Validation, Writing – original draft, Writing – review & editing
Affiliation Institute for Myelin and Glia Exploration, Jacobs School of Medicine and Biomedical Sciences, University at Buffalo—SUNY, Buffalo, New York, United States of America
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Jacob Favret ,
Contributed equally to this work with: Conlan Kreher, Jacob Favret
Roles Formal analysis, Investigation, Methodology, Validation, Writing – original draft, Writing – review & editing
Affiliation Department of Biotechnical and Clinical Laboratory Sciences, Jacobs School of Medicine and Biomedical Sciences, University at Buffalo—SUNY, Buffalo, New York, United States of America
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Nadav I. Weinstock,
Roles Conceptualization, Formal analysis, Funding acquisition, Investigation, Methodology, Validation, Writing – review & editing
Affiliations Institute for Myelin and Glia Exploration, Jacobs School of Medicine and Biomedical Sciences, University at Buffalo—SUNY, Buffalo, New York, United States of America, Department of Neurology, Jacobs School of Medicine and Biomedical Sciences, University at Buffalo—SUNY, Buffalo, New York, United States of America
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Malabika Maulik,
Roles Formal analysis, Validation
Affiliation Department of Biotechnical and Clinical Laboratory Sciences, Jacobs School of Medicine and Biomedical Sciences, University at Buffalo—SUNY, Buffalo, New York, United States of America
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Xinying Hong,
Roles Formal analysis
Affiliation Departments of Chemistry and Biochemistry, University of Washington, Seattle, Washington, United States of America
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Michael H. Gelb,
Roles Formal analysis, Writing – review & editing
Affiliation Departments of Chemistry and Biochemistry, University of Washington, Seattle, Washington, United States of America
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Lawrence Wrabetz,
Roles Conceptualization, Funding acquisition, Investigation, Supervision
Affiliations Institute for Myelin and Glia Exploration, Jacobs School of Medicine and Biomedical Sciences, University at Buffalo—SUNY, Buffalo, New York, United States of America, Department of Neurology, Jacobs School of Medicine and Biomedical Sciences, University at Buffalo—SUNY, Buffalo, New York, United States of America, Department of Biochemistry, Jacobs School of Medicine and Biomedical Sciences, University at Buffalo—SUNY, Buffalo, New York, United States of America
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M. Laura Feltri,
Roles Conceptualization, Data curation, Funding acquisition, Investigation, Methodology, Supervision, Writing – original draft, Writing – review & editing
Affiliations Institute for Myelin and Glia Exploration, Jacobs School of Medicine and Biomedical Sciences, University at Buffalo—SUNY, Buffalo, New York, United States of America, Department of Neurology, Jacobs School of Medicine and Biomedical Sciences, University at Buffalo—SUNY, Buffalo, New York, United States of America, Department of Biochemistry, Jacobs School of Medicine and Biomedical Sciences, University at Buffalo—SUNY, Buffalo, New York, United States of America
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Daesung Shin
Roles Conceptualization, Data curation, Formal analysis, Funding acquisition, Investigation, Methodology, Project administration, Resources, Software, Supervision, Validation, Visualization, Writing – original draft, Writing – review & editing
* E-mail: daesungs@buffalo.edu
Affiliations Institute for Myelin and Glia Exploration, Jacobs School of Medicine and Biomedical Sciences, University at Buffalo—SUNY, Buffalo, New York, United States of America, Department of Biotechnical and Clinical Laboratory Sciences, Jacobs School of Medicine and Biomedical Sciences, University at Buffalo—SUNY, Buffalo, New York, United States of America
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Neuron-specific ablation of the Krabbe disease gene galactosylceramidase in mice results in neurodegeneration
- Conlan Kreher,
- Jacob Favret,
- Nadav I. Weinstock,
- Malabika Maulik,
- Xinying Hong,
- Michael H. Gelb,
- Lawrence Wrabetz,
- M. Laura Feltri,
- Daesung Shin
- Published: July 5, 2022
- https://doi.org/10.1371/journal.pbio.3001661