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Open Access
Peer-reviewed
Research Article
Multiscale, Converging Defects of Macro-Porosity, Microstructure and Matrix Mineralization Impact Long Bone Fragility in NF1
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Jirko Kühnisch ,
* E-mail: jirko.kuehnisch@gmx.de (JK); kolanshy@molgen.mpg.de (MK)
Affiliations Institute for Medical Genetics and Human Genetics, Charité - Universitätsmedizin Berlin, Berlin, Germany, FG Development & Disease, Max Planck Institute for Molecular Genetics, Berlin, Germany
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Jong Seto,
Affiliations Department of Biomaterials, Max Planck Institute for Colloids and Interfaces, Potsdam, Germany, Department of Chemistry, Universität Konstanz, Konstanz, Germany
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Claudia Lange,
Affiliations Department of Biomaterials, Max Planck Institute for Colloids and Interfaces, Potsdam, Germany, Institut für Physiologische Chemie, MTZ, Medizinische Fakultät Carl Gustav Carus, Technische Universität Dresden, Dresden, Germany
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Susanne Schrof,
Affiliation Julius Wolff Institute & Brandenburg School of Regenerative Therapies, Charité - Universitätsmedizin Berlin, Berlin, Germany
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Sabine Stumpp,
Affiliation Institute for Medical Genetics and Human Genetics, Charité - Universitätsmedizin Berlin, Berlin, Germany
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Karolina Kobus,
Affiliation FG Development & Disease, Max Planck Institute for Molecular Genetics, Berlin, Germany
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Julia Grohmann,
Affiliation FG Development & Disease, Max Planck Institute for Molecular Genetics, Berlin, Germany
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Nadine Kossler,
Affiliation FG Development & Disease, Max Planck Institute for Molecular Genetics, Berlin, Germany
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Peter Varga,
Affiliation Julius Wolff Institute & Brandenburg School of Regenerative Therapies, Charité - Universitätsmedizin Berlin, Berlin, Germany
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Monika Osswald,
Affiliation FG Development & Disease, Max Planck Institute for Molecular Genetics, Berlin, Germany
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Denise Emmerich,
Affiliations Institute for Medical Genetics and Human Genetics, Charité - Universitätsmedizin Berlin, Berlin, Germany, FG Development & Disease, Max Planck Institute for Molecular Genetics, Berlin, Germany
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Sigrid Tinschert,
Affiliations Division für Humangenetik, Medizinische Universität Innsbruck, Innsbruck, Austria, Institut für Klinische Genetik, Medizinische Fakultät Carl Gustav Carus, Technische Universität Dresden, Dresden, Germany
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Falk Thielemann,
Affiliation Klinik für Orthopädie, Medizinische Fakultät Carl Gustav Carus, Technische Universität Dresden, Dresden, Germany
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Georg Duda,
Affiliations Julius Wolff Institute & Brandenburg School of Regenerative Therapies, Charité - Universitätsmedizin Berlin, Berlin, Germany, Berlin-Brandenburg Center for Regenerative Therapies, Berlin, Germany
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Wenke Seifert,
Affiliation Institute for Vegetative Anatomy, Charité - Universitätsmedizin Berlin, Berlin, Germany
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Thaqif el Khassawna,
Affiliation Laboratory of Experimental Trauma Surgery Giessen, Justus-Liebig University Giessen, Giessen, Germany
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David A. Stevenson,
Affiliation University of Utah, Department of Pediatrics, Division of Medical Genetics, Salt Lake City, Utah, United States of America
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Florent Elefteriou,
Affiliation Department of Medicine, Pharmacology and Cancer Biology, Center for Bone Biology, Vanderbilt University - Medical Center, Nashville, Tennessee, United States of America
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Uwe Kornak,
Affiliations Institute for Medical Genetics and Human Genetics, Charité - Universitätsmedizin Berlin, Berlin, Germany, FG Development & Disease, Max Planck Institute for Molecular Genetics, Berlin, Germany
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Kay Raum,
Affiliation Julius Wolff Institute & Brandenburg School of Regenerative Therapies, Charité - Universitätsmedizin Berlin, Berlin, Germany
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Peter Fratzl,
Affiliations Department of Biomaterials, Max Planck Institute for Colloids and Interfaces, Potsdam, Germany, Berlin-Brandenburg Center for Regenerative Therapies, Berlin, Germany
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Stefan Mundlos,
Affiliations Institute for Medical Genetics and Human Genetics, Charité - Universitätsmedizin Berlin, Berlin, Germany, FG Development & Disease, Max Planck Institute for Molecular Genetics, Berlin, Germany, Berlin-Brandenburg Center for Regenerative Therapies, Berlin, Germany
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Mateusz Kolanczyk
* E-mail: jirko.kuehnisch@gmx.de (JK); kolanshy@molgen.mpg.de (MK)
Affiliations Institute for Medical Genetics and Human Genetics, Charité - Universitätsmedizin Berlin, Berlin, Germany, FG Development & Disease, Max Planck Institute for Molecular Genetics, Berlin, Germany
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Multiscale, Converging Defects of Macro-Porosity, Microstructure and Matrix Mineralization Impact Long Bone Fragility in NF1
- Jirko Kühnisch,
- Jong Seto,
- Claudia Lange,
- Susanne Schrof,
- Sabine Stumpp,
- Karolina Kobus,
- Julia Grohmann,
- Nadine Kossler,
- Peter Varga,
- Monika Osswald
- Published: January 21, 2014
- https://doi.org/10.1371/journal.pone.0086115