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Open Access
Peer-reviewed
Research Article
Mitochondrial DNA Mutations Induce Mitochondrial Dysfunction, Apoptosis and Sarcopenia in Skeletal Muscle of Mitochondrial DNA Mutator Mice
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Asimina Hiona,
Current address: National Hellenic Research Foundation, Institute of Biological Research and Biotechnology, Athens, Greece
Affiliation Division of Biology of Aging, Department of Aging and Geriatric Research, Institute on Aging, College of Medicine, University of Florida, Gainesville, Florida, United States of America
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Alberto Sanz,
Affiliation Mitochondrial Gene Expression and Disease Group. Institute of Medical Technology and Tampere University Hospital, University of Tampere, Tampere, Finland
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Gregory C. Kujoth,
Affiliation Department of Genetics and Medical Genetics, University of Wisconsin, Madison, Wisconsin, United States of America
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Reinald Pamplona,
Affiliation Department of Experimental Medicine, University of Lleida-Institut de Recerca Biomèdica de Lleida, Lleida, Spain
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Arnold Y. Seo,
Affiliation Division of Biology of Aging, Department of Aging and Geriatric Research, Institute on Aging, College of Medicine, University of Florida, Gainesville, Florida, United States of America
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Tim Hofer,
Affiliation Division of Biology of Aging, Department of Aging and Geriatric Research, Institute on Aging, College of Medicine, University of Florida, Gainesville, Florida, United States of America
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Shinichi Someya,
Affiliations Department of Genetics and Medical Genetics, University of Wisconsin, Madison, Wisconsin, United States of America, Department of Applied Biological Chemistry, The University of Tokyo, Bunkyo-ku, Tokyo, Japan
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Takuya Miyakawa,
Affiliation Department of Applied Biological Chemistry, The University of Tokyo, Bunkyo-ku, Tokyo, Japan
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Chie Nakayama,
Affiliation Department of Applied Biological Chemistry, The University of Tokyo, Bunkyo-ku, Tokyo, Japan
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Alejandro K. Samhan-Arias,
Affiliation Department of Biochemistry and Molecular Biology, Faculty of Sciences, University of Extremadura, Badajoz, Spain
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Stephane Servais,
Affiliation Division of Biology of Aging, Department of Aging and Geriatric Research, Institute on Aging, College of Medicine, University of Florida, Gainesville, Florida, United States of America
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Jamie L. Barger,
Affiliation LifeGen Technologies, LLC, Madison, Wisconsin, United States of America
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Manuel Portero-Otín,
Affiliation Department of Experimental Medicine, University of Lleida-Institut de Recerca Biomèdica de Lleida, Lleida, Spain
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Masaru Tanokura,
Affiliation Department of Applied Biological Chemistry, The University of Tokyo, Bunkyo-ku, Tokyo, Japan
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Tomas A. Prolla ,
* E-mail: taprolla@wisc.edu (TAP); cleeuwen@aging.ufl.edu (CL)
Affiliation Department of Genetics and Medical Genetics, University of Wisconsin, Madison, Wisconsin, United States of America
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Christiaan Leeuwenburgh
* E-mail: taprolla@wisc.edu (TAP); cleeuwen@aging.ufl.edu (CL)
Affiliation Division of Biology of Aging, Department of Aging and Geriatric Research, Institute on Aging, College of Medicine, University of Florida, Gainesville, Florida, United States of America
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Mitochondrial DNA Mutations Induce Mitochondrial Dysfunction, Apoptosis and Sarcopenia in Skeletal Muscle of Mitochondrial DNA Mutator Mice
- Asimina Hiona,
- Alberto Sanz,
- Gregory C. Kujoth,
- Reinald Pamplona,
- Arnold Y. Seo,
- Tim Hofer,
- Shinichi Someya,
- Takuya Miyakawa,
- Chie Nakayama,
- Alejandro K. Samhan-Arias
- Published: July 7, 2010
- https://doi.org/10.1371/journal.pone.0011468