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Open Access
Peer-reviewed
Research Article
Mutant Human FUS Is Ubiquitously Mislocalized and Generates Persistent Stress Granules in Primary Cultured Transgenic Zebrafish Cells
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Jamie Rae Acosta,
Affiliations The Brain & Mind Research Institute, University of Sydney, Sydney, New South Wales, Australia, The Bosch Institute, University of Sydney, Sydney, New South Wales, Australia, Discipline of Anatomy and Histology, University of Sydney, Sydney, New South Wales, Australia
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Claire Goldsbury ,
* E-mail: claire.goldsbury@sydney.edu.au
Affiliations The Brain & Mind Research Institute, University of Sydney, Sydney, New South Wales, Australia, The Bosch Institute, University of Sydney, Sydney, New South Wales, Australia, Discipline of Anatomy and Histology, University of Sydney, Sydney, New South Wales, Australia
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Claire Winnick,
Affiliations The Bosch Institute, University of Sydney, Sydney, New South Wales, Australia, Discipline of Anatomy and Histology, University of Sydney, Sydney, New South Wales, Australia, Motorneurone Disease Research Centre, Australian School of Advanced Medicine, Macquarie University, Sydney, New South Wales, Australia
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Andrew P. Badrock,
Affiliations The Bosch Institute, University of Sydney, Sydney, New South Wales, Australia, Discipline of Anatomy and Histology, University of Sydney, Sydney, New South Wales, Australia, Motorneurone Disease Research Centre, Australian School of Advanced Medicine, Macquarie University, Sydney, New South Wales, Australia
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Stuart T. Fraser,
Affiliations The Bosch Institute, University of Sydney, Sydney, New South Wales, Australia, Discipline of Physiology, University of Sydney, Sydney, New South Wales, Australia
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Angela S. Laird,
Affiliations The Brain & Mind Research Institute, University of Sydney, Sydney, New South Wales, Australia, ANZAC Research Institute, University of Sydney, Sydney, New South Wales, Australia
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Thomas E. Hall,
Affiliation Institute for Molecular Bioscience, The University of Queensland, Brisbane, Australia
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Emily K. Don,
Affiliations The Bosch Institute, University of Sydney, Sydney, New South Wales, Australia, Motorneurone Disease Research Centre, Australian School of Advanced Medicine, Macquarie University, Sydney, New South Wales, Australia
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Jennifer A. Fifita,
Affiliations ANZAC Research Institute, University of Sydney, Sydney, New South Wales, Australia, Motorneurone Disease Research Centre, Australian School of Advanced Medicine, Macquarie University, Sydney, New South Wales, Australia
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Ian P. Blair,
Affiliations ANZAC Research Institute, University of Sydney, Sydney, New South Wales, Australia, Motorneurone Disease Research Centre, Australian School of Advanced Medicine, Macquarie University, Sydney, New South Wales, Australia
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Garth A. Nicholson,
Affiliations ANZAC Research Institute, University of Sydney, Sydney, New South Wales, Australia, Motorneurone Disease Research Centre, Australian School of Advanced Medicine, Macquarie University, Sydney, New South Wales, Australia
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Nicholas J. Cole
Affiliations The Bosch Institute, University of Sydney, Sydney, New South Wales, Australia, Discipline of Anatomy and Histology, University of Sydney, Sydney, New South Wales, Australia, Motorneurone Disease Research Centre, Australian School of Advanced Medicine, Macquarie University, Sydney, New South Wales, Australia
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Mutant Human FUS Is Ubiquitously Mislocalized and Generates Persistent Stress Granules in Primary Cultured Transgenic Zebrafish Cells
- Jamie Rae Acosta,
- Claire Goldsbury,
- Claire Winnick,
- Andrew P. Badrock,
- Stuart T. Fraser,
- Angela S. Laird,
- Thomas E. Hall,
- Emily K. Don,
- Jennifer A. Fifita,
- Ian P. Blair
- Published: June 9, 2014
- https://doi.org/10.1371/journal.pone.0090572