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Open Access
Peer-reviewed
Research Article
Multiple Organ System Defects and Transcriptional Dysregulation in the Nipbl+/− Mouse, a Model of Cornelia de Lange Syndrome
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Shimako Kawauchi ,
Contributed equally to this work with: Shimako Kawauchi, Anne L. Calof
Affiliations Department of Anatomy and Neurobiology, University of California Irvine, Irvine, California, United States of America, Developmental Biology Center, University of California Irvine, Irvine, California, United States of America, Center for Hearing Research, University of California Irvine, Irvine, California, United States of America
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Anne L. Calof ,
Contributed equally to this work with: Shimako Kawauchi, Anne L. Calof
* E-mail: alcalof@uci.edu (ALC); adlander@uci.edu (ADL)
Affiliations Department of Anatomy and Neurobiology, University of California Irvine, Irvine, California, United States of America, Developmental Biology Center, University of California Irvine, Irvine, California, United States of America, Center for Hearing Research, University of California Irvine, Irvine, California, United States of America, Center for Complex Biological Systems, University of California Irvine, Irvine, California, United States of America
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Rosaysela Santos,
Affiliations Department of Anatomy and Neurobiology, University of California Irvine, Irvine, California, United States of America, Developmental Biology Center, University of California Irvine, Irvine, California, United States of America
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Martha E. Lopez-Burks,
Affiliations Developmental Biology Center, University of California Irvine, Irvine, California, United States of America, Department of Developmental and Cell Biology, University of California Irvine, Irvine, California, United States of America
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Clint M. Young,
Affiliations Department of Anatomy and Neurobiology, University of California Irvine, Irvine, California, United States of America, Developmental Biology Center, University of California Irvine, Irvine, California, United States of America
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Michelle P. Hoang,
Affiliations Developmental Biology Center, University of California Irvine, Irvine, California, United States of America, Department of Developmental and Cell Biology, University of California Irvine, Irvine, California, United States of America
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Abigail Chua,
Affiliations Developmental Biology Center, University of California Irvine, Irvine, California, United States of America, Department of Developmental and Cell Biology, University of California Irvine, Irvine, California, United States of America
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Taotao Lao,
Affiliation Department of Bioscience and Biotechnology, Drexel University, Philadelphia, Pennsylvania, United States of America
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Mark S. Lechner,
Affiliation Department of Bioscience and Biotechnology, Drexel University, Philadelphia, Pennsylvania, United States of America
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Jeremy A. Daniel,
Affiliation National Cancer Institute, National Institutes of Health, Bethesda, Maryland, United States of America
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Andre Nussenzweig,
Affiliation National Cancer Institute, National Institutes of Health, Bethesda, Maryland, United States of America
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Leonard Kitzes,
Affiliations Department of Anatomy and Neurobiology, University of California Irvine, Irvine, California, United States of America, Center for Hearing Research, University of California Irvine, Irvine, California, United States of America
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Kyoko Yokomori,
Affiliation Department of Biological Chemistry, University of California Irvine, Irvine, California, United States of America
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Benedikt Hallgrimsson,
Affiliation Department of Cell Biology and Anatomy, University of Calgary, Calgary, Alberta, Canada
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Arthur D. Lander
* E-mail: alcalof@uci.edu (ALC); adlander@uci.edu (ADL)
Affiliations Developmental Biology Center, University of California Irvine, Irvine, California, United States of America, Center for Complex Biological Systems, University of California Irvine, Irvine, California, United States of America, Department of Developmental and Cell Biology, University of California Irvine, Irvine, California, United States of America
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Multiple Organ System Defects and Transcriptional Dysregulation in the Nipbl+/− Mouse, a Model of Cornelia de Lange Syndrome
- Shimako Kawauchi,
- Anne L. Calof,
- Rosaysela Santos,
- Martha E. Lopez-Burks,
- Clint M. Young,
- Michelle P. Hoang,
- Abigail Chua,
- Taotao Lao,
- Mark S. Lechner,
- Jeremy A. Daniel
- Published: September 18, 2009
- https://doi.org/10.1371/journal.pgen.1000650